Pulmonary Fibrosis NIWhat is Pulmonary Fibrosis.

Learn MoreWhat is Pulmonary Fibrosis.

The word “pulmonary” means lung and the word “fibrosis” means scar tissue— similar to scars that you may have on your skin from an old injury or surgery. So, in its simplest sense, pulmonary fibrosis (PF) means scarring in the lungs. Over time, the scar tissue can destroy the normal lung and make it hard for oxygen to get into your blood. Low oxygen levels (and the stiff scar tissue itself) can cause you to feel short of breath, particularly when walking and exercising. Pulmonary fibrosis isn’t just one disease. It is a family of more than 200 different lung diseases that all look very much alike. The PF family of lung diseases falls into an even larger group of diseases called the interstitial lung diseases (also known as ILD), which includes all of the diseases that have inflammation and/or scarring in the lung. Some interstitial lung diseases don’t include scar tissue. When an interstitial lung disease does include scar tissue in the lung, we call it pulmonary fibrosis. IPF is a form of interstitial lung disease, primarily involving the interstitium (the tissue and space around the air sacs of the lungs), and not directly affecting the airways or blood vessels. There are many other kinds of interstitial lung disease that can also cause inflammation and/or fibrosis, and these are treated differently. It is important to work with your doctor to determine if you have IPF or another form of interstitial lung disease.

Learn MoreWhat causes Pulmonary Fibrosis.



Up to 20% of people with IPF have another family member with an interstitial lung disease


Male genetics have a large part to play. Approximately 75% of patients with IPF are male


Approximately 75% of people with IPF are current or previous cigarette smokers.


Research across the UK and rest of the world shows almost all patients with IPF are over the age of 50 years

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Typically called hypersensitivity pneumonitis (HP) or chronic hypersensitivity pneumonitis. HP occurs when the lungs react with inflammation and scarring after breathing in mold spores, bacteria, animal proteins (especially from indoor or caged birds), or other known triggers. No one is certain why some people are so susceptible to developing HP and others are not.

Learn MoreSymptoms of Pulmonary Fibrosis.


Shortness of Breath

The most common symptom of pulmonary fibrosis is shortness of breath

Loss of Appetite

With a lack of Oxygen, sufferers may start to experience less desire to eat and weight loss follows

Dry Cough

One of the most common symptoms of pulmonary fibrosis is a dry, persistent cough


Clubbing is a thickening of the flesh under the fingernails, causing the nails to curve downward

VideoLife with Pulmonary Fibrosis.

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